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p class=“engage”>Hey there, health enthusiasts! Today, I want to talk about something that might interest you – Phenylalanine Hydroxylase. This amazing protein has the unique ability to break down phenylalanine, an essential amino acid that our bodies cannot produce. If you’re unfamiliar with it, phenylalanine is found in most high-protein foods like milk, eggs, and meat. Our body needs it to produce many important molecules, but too much of it can be harmful. That’s where Phenylalanine Hydroxylase comes in – it converts the excess phenylalanine into another amino acid called tyrosine, which is used to make important neurotransmitters like dopamine and adrenaline. However, some people have a genetic mutation that makes their Phenylalanine Hydroxylase enzyme less effective, leading to a condition called Phenylketonuria (PKU). In PKU patients, excess phenylalanine and its by-products can build up in the blood and cause damage to the brain and nervous system. That’s why early diagnosis and treatment are critical for these individuals. Now, let’s take a closer look at these amazing images showcasing Phenylalanine Hydroxylase. In the first image, we see a detailed schematic of the reaction carried out by this enzyme. As you can see, it involves the conversion of phenylalanine to tyrosine with the help of oxygen and tetrahydrobiopterin (BH4), a cofactor that is essential for the enzyme’s activity. The second image depicts the devastating effects of PKU on the brain, with the yellow areas indicating severe damage. It’s a sobering reminder of how important it is to maintain a healthy balance of amino acids in our bodies. To sum it up, Phenylalanine Hydroxylase is an incredible enzyme that plays a crucial role in our bodies. It allows us to metabolize an essential amino acid while preventing toxic build-up in our bodies. Unfortunately, some people are not able to produce enough of this enzyme, leading to a condition called PKU. I hope this little introduction has helped you appreciate the role of this amazing protein in our bodies. Stay healthy, folks! Thanks for tuning in.
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Brain damage in PKU patients
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Phenylketonuria - The Lancet
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